Acroangiodermatitis of Mali and Stewart-Bluefarb syndrome.

Acroangiodermatitis of Mali and Stewart-Bluefarb syndrome.

Chea, Emily P;Rutt, Veronica L;Levin, Joshua;McClain, Richard;Purcell, Stephen M;
cutis 2019 Vol. 103 pp. 336-339
171
chea2019acroangiodermatitiscutis

Abstract

Acroangiodermatitis (AAD), also known as pseudo-Kaposi sarcoma, is a rare benign vascular proliferation mainly of the extremities. It is characterized by violaceous patches or plaques resembling Kaposi sarcoma. The term pseudo-Kaposi sarcoma encompasses 2 variants of acroangiodermatitis: Mali type and Stewart-Bluefarb syndrome (SBS). Mali-type AAD is more common and is associated with chronic venous hypertension, while SBS is more rare and is associated with arteriovenous malformations and iatrogenic arteriovenous fistulae. We report 2 patients, representing each type of AAD.

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